Wise Young
08-10-2005, 02:16 PM
Should ventilation be instituted in children with SMA1. This is a horrendous motoneuroal degeneration disease with almost 100% mortality rate by age 2.
Bush A, Fraser J, Jardine E, Paton J, Simonds A and Wallis C (2005). Respiratory management of the infant with type 1 spinal muscular atrophy. Arch Dis Child 90: 709-11. A recent paper has highlighted the differences in the respiratory management offered to infants with type 1 spinal muscular atrophy (SMA-1). Current views appear polarised between those who would offer nothing, to those who would proceed as far even as tracheostomy and long term invasive ventilation for these infants. Here we offer a personal view, as a possible template for managing a vexed and emotional problem. The complex non-respiratory aspects of the holistic care of these infants will not be discussed. Royal Brompton Hospital, Sydney Street, London SW3 6NP, UK. a.bush@rbh.nthames.nhs.uk http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=PubMed&dopt=Citation&list_uids=15970612
Bush A, Fraser J, Jardine E, Paton J, Simonds A and Wallis C (2005). Respiratory management of the infant with type 1 spinal muscular atrophy. Arch Dis Child 90: 709-11. A recent paper has highlighted the differences in the respiratory management offered to infants with type 1 spinal muscular atrophy (SMA-1). Current views appear polarised between those who would offer nothing, to those who would proceed as far even as tracheostomy and long term invasive ventilation for these infants. Here we offer a personal view, as a possible template for managing a vexed and emotional problem. The complex non-respiratory aspects of the holistic care of these infants will not be discussed. Royal Brompton Hospital, Sydney Street, London SW3 6NP, UK. a.bush@rbh.nthames.nhs.uk http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=PubMed&dopt=Citation&list_uids=15970612